raskazhite about fenilketonurija
Dr Hannibal Lexter
06.07.2004, 16:35
Otnositsya k gruppe bolezney svyazanix s narusheniem obmena aminokislot. PKU (phenylketonuria) svyazana s narusheniem perevoda phenylalanina v tyrozin. V rezulktate phenilalanin perevoditsya v phebylpyritic kislotu, kotoraya nakaplivaetsya. Esli ne lechit to u bolnix nabludaetsya zaderzka umstvennogo razvitiya, eczemi, epilepsiya-podobnie pristupi. Lechenie na segodnya eto umenshenie phenylalanina v diete.
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